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Medientyp
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Autor/in
- Braulke, Thomas
- Pohl, Sandra 22
- Storch, Stephan 12
- Ullrich, Kurt 12
- Schweizer, Michaela 11
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72 Einträge gefunden
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Early enzyme replacement therapy prevents dental and craniofacial abnormalities in a mouse model of mucopolysaccharidosis type VI
- Nagpal, Rohit
- Georgi, Gina
- Knauth, Sarah
- Schmid-Herrmann, Carmen
- Muschol, Nicole
- Braulke, Thomas
- Kahl-Nieke, Bärbel
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Influenza binds phosphorylated glycans from human lung
- Byrd-Leotis, Lauren
- Jia, Nan
- Dutta, Sucharita
- Trost, Jessica F
- Gao, Chao
- Cummings, Sandra F
- Braulke, Thomas
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Quantitative Proteome Analysis of Mouse Liver Lysosomes Provides Evidence for Mannose 6-phosphate-independent Targeting Mechanisms of Acid Hydrolases in Mucolipidosis II
- Markmann, Sandra
- Krambeck, Svenja
- Hughes, Christopher J
- Mirzaian, Mina
- Aerts, Johannes M F G
- Saftig, Paul
- Schweizer, Michaela
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Site-1 protease and lysosomal homeostasis
- Velho, Renata Voltolini
- De Pace, Raffaella
- Klünder, Sarah
- Di Lorenzo, Giorgia
- Schweizer, Michaela
- Braulke, Thomas
- Pohl, Sandra
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Disease-causing mutations affecting surface residues of mitochondrial glutaryl-CoA dehydrogenase impair stability, heteromeric complex formation, and mitochondria architecture
- Schmiesing, Jessica
- Lohmöller, Benjamin
- Schweizer, Michaela
- Tidow, Henning
- Gersting, Søren W
- Muntau, Ania C
- Braulke, Thomas
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Identification of the interaction domains between alpha- and gamma-subunits of GlcNAc-1-phosphotransferase
2016 - Forschungsinformationssystem der UHH -
Single-chain antibody-fragment M6P-1 possesses a mannose 6-phosphate monosaccharide-specific binding pocket that distinguishes N-glycan phosphorylation in a branch-specific manner
- Blackler, Ryan J.
- Evans, Dylan W.
- Smith, David F.
- Cummings, Richard D.
- Brooks, Cory L.
- Braulke, Thomas
- Liu, Xinyu
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Sustained Neural Stem Cell-Based Intraocular Delivery of CNTF Attenuates Photoreceptor Loss in the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis
- Jankowiak, Wanda
- Kruszewski, Katharina
- Flachsbarth, Kai
- Skevas, Christos
- Richard, Gisbert
- Rüther, Klaus
- Braulke, Thomas
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Site-1 protease-activated formation of lysosomal targeting motifs is independent of the lipogenic transcription control
2015 - Forschungsinformationssystem des UKE -
Analyses of disease-related GNPTAB mutations define a novel GlcNAc-1-phosphotransferase interaction domain and an alternative site-1 protease cleavage site
- Velho, Renata Voltolini
- De Pace, Raffaella
- Klünder, Sarah
- Sperb-Ludwig, Fernanda
- Lourenço, Charles Marques
- Schwartz, Ida V D
- Braulke, Thomas
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Subunit interactions of the disease-related hexameric GlcNAc-1-phosphotransferase complex
- De Pace, Raffaella
- Voltolini Velho, Renata
- Encarnação, Marisa
- Marschner, Katrin
- Braulke, Thomas
- Pohl, Sandra
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Mannose 6-phosphate-independent Lysosomal Sorting of LIMP-2.
- Blanz, Judith
- Zunke, Friederike
- Markmann, Sandra
- Damme, Markus
- Braulke, Thomas
- Saftig, Paul
- Schwake, Michael
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Mannose 6 phosphorylation of lysosomal enzymes controls B cell functions
- Otomo, Takanobu
- Schweizer, Michaela
- Kollmann, Katrin
- Schumacher, Valéa
- Muschol, Nicole
- Tolosa, Eva
- Mittrücker, Hans-Willi
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Mucolipidosis II-related mutations inhibit the exit from the endoplasmic reticulum and proteolytic cleavage of GlcNAc-1-phosphotransferase precursor protein (GNPTAB)
- De Pace, Raffaella
- Coutinho, Maria Francisca
- Nolte, Friedrich
- Haag, Friedrich
- Prata, Maria João
- Alves, Sandra
- Braulke, Thomas
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Interaction of glutaric aciduria type 1-related glutaryl-CoA dehydrogenase with mitochondrial matrix proteins
2014 - Forschungsinformationssystem des UKE - frei zugänglich