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- Krämer, Elisabeth
- Schlossarek, Saskia 9
- Carrier, Lucie 8
- Mearini, Giulia 7
- Geertz, Birgit 5
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22 Einträge gefunden
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Disease modeling of a mutation in α-actinin 2 guides clinical therapy in hypertrophic cardiomyopathy - Addendum
- Prondzynski, Maksymilian
- Lemoine, Marc D
- Zech, Antonia Tl
- Horváth, András
- Di Mauro, Vittoria
- Koivumäki, Jussi T
- Kresin, Nico
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A Transgenic Mouse Model of Eccentric Left Ventricular Hypertrophy With Preserved Ejection Fraction Exhibits Alterations in the Autophagy-Lysosomal Pathway
- Wenzel, Kristin
- Krämer, Elisabeth
- Geertz, Birgit
- Carrier, Lucie
- Felix, Stephan B
- Könemann, Stephanie
- Schlossarek, Saskia
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A Novel miRNA Screen Identifies miRNA-4454 as a Candidate Biomarker for Ventricular Fibrosis in Patients with Hypertrophic Cardiomyopathy
2021 - Forschungsinformationssystem des UKE - frei zugänglich -
Generation of bi-allelic MYBPC3 truncating mutant and isogenic control from an iPSC line of a patient with hypertrophic cardiomyopathy
- Warnecke, Nele Annika
- Ulmer, Bärbel M
- Laufer, Sandra D
- Shibamiya, Aya
- Krämer, Elisabeth
- Neuber, Christiane
- Hanke, Sophia
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Analysis of Contractile Function of Permeabilized Human Hypertrophic Cardiomyopathy Multicellular Heart Tissue
- Kresin, Nico
- Stücker, Sabrina
- Krämer, Elisabeth
- Flenner, Frederik
- Mearini, Giulia
- Münch, Julia
- Patten, Monica
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Disease modeling of a mutation in α-actinin 2 guides clinical therapy in hypertrophic cardiomyopathy
- Prondzynski, Maksymilian
- Lemoine, Marc D
- Zech, Antonia Theresa Luisa
- Horvath, Andras
- Di Mauro, Vittoria
- Koivumäki, Jussi T
- Kresin, Nico
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S100A4 as a target of the E3-ligase Asb2β and its effect on engineered heart tissue
- Braumann, Simon
- Thottakara, Tilo
- Stücker, Sabrina
- Reischmann-Düsener, Silke
- Krämer, Elisabeth
- Groß, Julia
- Hirt, Marc
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Blinded contractility analysis in hiPSC-cardiomyocytes in engineered heart tissue format: Comparison with human atrial trabeculae
- Mannhardt, Ingra
- Eder, Alexandra
- Dumotier, Berengere
- Prondzynski, Maksymilian
- Krämer, Elisabeth
- Traebert, Martin
- Söhren, Klaus-Dieter
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Evaluation of MYBPC3 trans-Splicing and Gene Replacement as Therapeutic Options in Human iPSC-Derived Cardiomyocytes
- Prondzynski, Maksymilian
- Krämer, Elisabeth
- Laufer, Sandra
- Domke-Shibamiya, Aya
- Pless, Ole
- Flenner, Frederik
- Müller, Oliver J
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Serum Matrix Metalloproteinases as Quantitative Biomarkers for Myocardial Fibrosis and Sudden Cardiac Death Risk Stratification in Patients With Hypertrophic Cardiomyopathy
- Münch, Julia
- Avanesov, Maxim
- Bannas, Peter
- Säring, Dennis
- Krämer, Elisabeth
- Mearini, Giulia
- Carrier, Lucie
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The E3 ubiquitin ligase Asb2β is downregulated in a mouse model of hypertrophic cardiomyopathy and targets desmin for proteasomal degradation
- Thottakara, Tilo
- Friedrich, Felix W
- Reischmann, Silke
- Braumann, Simon
- Schlossarek, Saskia
- Krämer, Elisabeth
- Juhr, Denise
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Mybpc3 gene therapy for neonatal cardiomyopathy enables long-term disease prevention in mice
- Mearini, Giulia
- Stimpel, Doreen
- Geertz, Birgit
- Weinberger, Florian
- Krämer, Elisabeth
- Schlossarek, Saskia
- Mourot-Filiatre, Julia
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Repair of Mybpc3 mRNA by 5'-trans-splicing in a Mouse Model of Hypertrophic Cardiomyopathy
- Mearini, Giulia
- Stimpel, Doreen
- Krämer, Elisabeth
- Geertz, Birgit
- Braren, Ingke
- Hornung, Christina
- Précigout, Guillaume
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BSE-associated prion-amyloid cardiomyopathy in primates
- Krasemann, Susanne
- Mearini, Giulia
- Krämer, Elisabeth
- Wagenführ, Katja
- Schulz-Schaeffer, Walter
- Neumann, Melanie
- Bodemer, Walter
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Increased myofilament Ca2+ sensitivity and diastolic dysfunction as early consequences of Mybpc3 mutation in heterozygous knock-in mice.
- Fraysse, Bodvaël
- Weinberger, Florian
- Bardswell, Sonya C
- Cuello, Friedericke
- Vignier, Nicolas
- Geertz, Birgit
- Starbatty, Jutta
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Atrogin-1 and MuRF1 regulate cardiac MyBP-C levels via different mechanisms.
- Mearini, Giulia
- Hornung, Christina
- Schlossarek, Saskia
- Witt, Christian C
- Krämer, Elisabeth
- Cao, Peirang
- Gomes, Marcelo D
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Nonsense-mediated mRNA decay and ubiquitin-proteasome system regulate cardiac myosin-binding protein C mutant levels in cardiomyopathic mice.
- Vignier, Nicolas
- Schlossarek, Saskia
- Fraysse, Bodvael
- Mearini, Giulia
- Krämer, Elisabeth
- Pointu, Hervé
- Mougenot, Nathalie