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Medientyp
- Text 20
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Erscheinungsjahr
Autor/in
- Damme, Markus
- Saftig, Paul 6
- Braulke, Thomas 5
- Lüllmann-Rauch, Renate 5
- Schweizer, Michaela 5
- alle zeigen
Sprache
- Englisch 20
20 Einträge gefunden
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Anchorless risk or released benefit?:An updated view on the ADAM10-mediated shedding of the prion protein
- Mohammadi, Behnam
- Song, Feizhi
- Matamoros-Angles, Andreu
- Shafiq, Mohsin
- Damme, Markus
- Puig, Berta
- Glatzel, Markus
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Lack of a protective effect of the Tmem106b "protective SNP" in the Grn knockout mouse model for frontotemporal lobar degeneration
- Cabron, Anne-Sophie
- Borgmeyer, Uwe
- Richter, Julia
- Peisker, Helga
- Gutbrod, Katharina
- Dörmann, Peter
- Capell, Anja
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Ligands binding to the prion protein induce its proteolytic release with therapeutic potential in neurodegenerative proteinopathies
- Linsenmeier, Luise
- Mohammadi, Behnam
- Shafiq, Mohsin
- Frontzek, Karl
- Bär, Julia
- Shrivastava, Amulya N
- Damme, Markus
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Ligands binding to the prion protein induce its proteolytic release with therapeutic potential in neurodegenerative proteinopathies
- Linsenmeier, Luise
- Mohammadi, Behnam
- Shafiq, Mohsin
- Frontzek, Karl
- Bär, Julia
- Shrivastava, Amulya N.
- Damme, Markus
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Enzyme replacement therapy with recombinant pro-CTSD (cathepsin D) corrects defective proteolysis and autophagy in neuronal ceroid lipofuscinosis
- Marques, André R A
- Di Spiezio, Alessandro
- Thießen, Niklas
- Schmidt, Lina
- Grötzinger, Joachim
- Lüllmann-Rauch, Renate
- Damme, Markus
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The lysosomal transporter MFSD1 is essential for liver homeostasis and critically depends on its accessory subunit GLMP
- Massa López, David
- Thelen, Melanie
- Stahl, Felix
- Thiel, Christian
- Linhorst, Arne
- Sylvester, Marc
- Hermanns-Borgmeyer, Irm
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Unconventional Trafficking of Mammalian Phospholipase D3 to Lysosomes
- Gonzalez, Adriana Carolina
- Schweizer, Michaela
- Jagdmann, Sebastian
- Bernreuther, Christian
- Reinheckel, Thomas
- Saftig, Paul
- Damme, Markus
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RNase H2 Loss in Murine Astrocytes Results in Cellular Defects Reminiscent of Nucleic Acid-Mediated Autoinflammation
- Bartsch, Kareen
- Damme, Markus
- Regen, Tommy
- Becker, Lore
- Garrett, Lillian
- Hölter, Sabine M
- Knittler, Katharina
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Quantitative Proteome Analysis of Mouse Liver Lysosomes Provides Evidence for Mannose 6-phosphate-independent Targeting Mechanisms of Acid Hydrolases in Mucolipidosis II
- Markmann, Sandra
- Krambeck, Svenja
- Hughes, Christopher J
- Mirzaian, Mina
- Aerts, Johannes M F G
- Saftig, Paul
- Schweizer, Michaela
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A mouse model for fucosidosis recapitulates storage pathology and neurological features of the milder form of the human disease
- Wolf, Heike
- Damme, Markus
- Stroobants, Stijn
- D'Hooge, Rudi
- Beck, Hans Christian
- Hermans-Borgmeyer, Irm
- Lüllmann-Rauch, Renate
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Degeneration of Photoreceptor Cells in Arylsulfatase G-Deficient Mice
2016 - Forschungsinformationssystem des UKE - frei zugänglich -
Mannose 6-phosphate-independent Lysosomal Sorting of LIMP-2.
- Blanz, Judith
- Zunke, Friederike
- Markmann, Sandra
- Damme, Markus
- Braulke, Thomas
- Saftig, Paul
- Schwake, Michael
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In Vivo Evidence for Lysosome Depletion and Impaired Autophagic Clearance in Hereditary Spastic Paraplegia Type SPG11
- Varga , Rita-Eva
- Khundadze, Mukhran
- Damme, Markus
- Nietzsche, Sandor
- Hoffmann, Birgit
- Stauber, Tobias
- Koch, Nicole
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Gene disruption of Mfsd8 in mice provides the first animal model for CLN7 disease
- Damme, Markus
- Brandenstein, Laura
- Fehr, Susanne
- Jankowiak, Wanda
- Bartsch, Udo
- Schweizer, Michaela
- Hermans-Borgmeyer, Irm
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Mannose 6-dephosphorylation of lysosomal proteins mediated by acid phosphatases Acp2 and Acp5
- Makrypidi, Georgia
- Damme, Markus
- Müller-Loennies, Sven
- Trusch, Maria
- Schlüter, Hartmut
- Heeren, Jörg
- Lübke, Torben
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Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosis.
- Thelen, Melanie
- Damme, Markus
- Daμμe, Markus
- Schweizer, Michaela
- Hagel, Christian
- Wong, Andrew M S
- Cooper, Jonathan D