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- Bartsch, Udo
- Jankowiak, Wanda 11
- Richard, Gisbert 9
- Bartsch, Susanne 6
- Flachsbarth, Kai 6
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37 Einträge gefunden
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Ongoing retinal degeneration despite intraventricular enzyme replacement therapy with cerliponase alfa in late-infantile neuronal ceroid lipofuscinosis type 2 (CLN2 disease)
- Dulz, Simon
- Schwering, C
- Wildner, Jan
- Spartalis, Christoph
- Schuettauf, Frank
- Bartsch, Udo
- Wibbeler, Eva
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Intravitreal gene therapy restores the autophagy-lysosomal pathway and attenuates retinal degeneration in cathepsin D-deficient mice
- Liu, Junling
- Bassal, Mahmoud
- Schlichting, Stefanie
- Braren, Ingke
- Di Spiezio, Alessandro
- Saftig, Paul
- Bartsch, Udo
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Multiple Na,K-ATPase Subunits Colocalize in the Brush Border of Mouse Choroid Plexus Epithelial Cells
- Baasch Christensen, Inga
- Cheng, Lei
- Brewer, Jonathan R
- Bartsch, Udo
- Fenton, Robert A
- H Damkier, Helle
- Praetorius, Jeppe
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Cell-Based Neuroprotection of Retinal Ganglion Cells in Animal Models of Optic Neuropathies
2021 - Forschungsinformationssystem des UKE - frei zugänglich -
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Rapid and Progressive Loss of Multiple Retinal Cell Types in Cathepsin D-Deficient Mice - An Animal Model of CLN10 Disease
2021 - Forschungsinformationssystem des UKE - frei zugänglich -
Intravitreal Co-Administration of GDNF and CNTF Confers Synergistic and Long-Lasting Protection against Injury-Induced Cell Death of Retinal Ganglion Cells in Mice
- Dulz, Simon
- Bassal, Mahmoud
- Flachsbarth, Kai
- Riecken, Kristoffer
- Fehse, Boris
- Schlichting, Stefanie
- Bartsch, Susanne
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An ophthalmic rating scale to assess ocular involvement in juvenile CLN3 disease
- Dulz, Simon
- Atiskova, Yevgeniya
- Wibbeler, Eva
- Wildner, Jan Einar
- Wagenfeld, Lars
- Schwering, Christoph
- Nickel, Miriam
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Mice deficient in the lysosomal enzyme palmitoyl-protein thioesterase 1 (PPT1) display a complex retinal phenotype
- Atiskova, Yevgeniya
- Bartsch, Susanne
- Danyukova, Tatyana
- Becker, Elke
- Hagel, Christian
- Storch, Stephan
- Bartsch, Udo
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Current and Emerging Treatment Strategies for Neuronal Ceroid Lipofuscinoses
2019 - Forschungsinformationssystem des UKE -
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Retinal Degeneration in Mice Deficient in the Lysosomal Membrane Protein CLN7
2016 - Forschungsinformationssystem des UKE - frei zugänglich -
Degeneration of Photoreceptor Cells in Arylsulfatase G-Deficient Mice
2016 - Forschungsinformationssystem des UKE - frei zugänglich -
Sustained Neural Stem Cell-Based Intraocular Delivery of CNTF Attenuates Photoreceptor Loss in the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis
- Jankowiak, Wanda
- Kruszewski, Katharina
- Flachsbarth, Kai
- Skevas, Christos
- Richard, Gisbert
- Rüther, Klaus
- Braulke, Thomas
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Neural stem cell-based intraocular administration of ciliary neurotrophic factor attenuates the loss of axotomized ganglion cells in adult mice
- Flachsbarth, Kai
- Kruszewski, Katharina
- Jung, Gila
- Jankowiak, Wanda
- Riecken, Kristoffer
- Wagenfeld, Lars
- Richard, Gisbert
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Gene disruption of Mfsd8 in mice provides the first animal model for CLN7 disease
- Damme, Markus
- Brandenstein, Laura
- Fehr, Susanne
- Jankowiak, Wanda
- Bartsch, Udo
- Schweizer, Michaela
- Hermans-Borgmeyer, Irm