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- Braulke, Thomas
- Pohl, Sandra 22
- Storch, Stephan 12
- Ullrich, Kurt 12
- Schweizer, Michaela 11
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72 Einträge gefunden
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Apoptotic photoreceptor loss and altered expression of lysosomal proteins in the nclf mouse model of neuronal ceroid lipofuscinosis
- Bartsch, Udo
- Galliciotti, Giovanna
- Jofre, Guillermo F
- Jankowiak, Wanda
- Hagel, Christian
- Braulke, Thomas
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Ultrastructural analysis of neuronal and non-neuronal lysosomal storage in mucolipidosis type II knock-in mice
2013 - Forschungsinformationssystem des UKE -
Mass spectrometric analysis of neutral and anionic N-glycans from a Dictyostelium discoideum model for human congenital disorder of glycosylation CDG IL.
- Hykollari, Alba
- Balog, Crina I A
- Rendić, Dubravko
- Braulke, Thomas
- Wilson, Iain B H
- Paschinger, Katharina
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I-cell disease and Pseudo-Hurler Polydystrophy: Disorders of lysosomal enzyme phosphorylation and localization
2013 - Forschungsinformationssystem des UKE -
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Cell biology and function of neuronal ceroid lipofuscinosis-related proteins
2013 - Forschungsinformationssystem des UKE -
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Mannose 6-dephosphorylation of lysosomal proteins mediated by acid phosphatases Acp2 and Acp5
- Makrypidi, Georgia
- Damme, Markus
- Müller-Loennies, Sven
- Trusch, Maria
- Schlüter, Hartmut
- Heeren, Jörg
- Lübke, Torben
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Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosis.
- Thelen, Melanie
- Damme, Markus
- Daμμe, Markus
- Schweizer, Michaela
- Hagel, Christian
- Wong, Andrew M S
- Cooper, Jonathan D
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Glutaric aciduria type 1 metabolites impair the succinate transport from astrocytic to neuronal cells.
2011 - Forschungsinformationssystem des UKE -
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N-glycans and glycosylphosphatidylinositol-anchor act on polarized sorting of mouse PrP(C) in Madin-Darby canine kidney cells.
- Puig Martorell, Berta
- Altmeppen, Hermann C.
- Thurm, Dana Kathrin
- Geissen, Markus
- Conrad, Catharina
- Braulke, Thomas
- Glatzel, Markus
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Post-translational modifications of the γ-subunit affect intracellular trafficking and complex assembly of GlcNAc-1-phosphotransferase
2011 - Forschungsinformationssystem der UHH - frei zugänglich -